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ID

http://id.who.int/icd/entity/1446983705

Preferred Name

Pachyonychie

Definitions

Pachyonychia congenita is a rare genodermatosis predominantly featuring painful palmoplantar keratoderma, thickened nails, cysts and whitish oral mucosa.

Type

http://www.w3.org/2002/07/owl#Class

comment

Pachyonychia congenita is a rare genodermatosis predominantly featuring painful palmoplantar keratoderma, thickened nails, cysts and whitish oral mucosa.

pachyonychia congenita jest rzadki geneodermatosis głównie featuring bolesne palmoplantar keratoderma, zagęszczone paznokcie, torbiele i białawej błony śluzowej jamy ustnej.

Pachyonychia congenita ist eine seltene Genodermatose, die überwiegend schmerzhafte palmoplantäre Keratodermie, verdickte Nägel, Zysten und weißliche Mundschleimhaut aufweist.

pachyonychia congenita είναι ένα σπάνιο genodermatosis κυρίως που χαρακτηρίζει επώδυνη palmoplantar keratoderma, πυκνά νύχια, κύστεις και υπόλευκο βλεννογόνο.

pachyonychia congenita est une génodermatose rare qui se caractérise principalement par une kératodermie palmoplantaire douloureuse, des ongles épaissis, des kystes et de la muqueuse buccale blanchâtre.

broaderTransitive

http://id.who.int/icd/entity/1819307779

http://id.who.int/icd/entity/1339615175

http://id.who.int/icd/entity/1283926457

prefLabel

Pachyonychie

browserUrl

NA

label

Pachyonychia congenita

pachyonychia congenita

Pachyonychie

pachyonychia τους

Pachyonychia congenita

Pachyonychie congénitale

subClassOf

http://id.who.int/icd/entity/1819307779

http://id.who.int/icd/entity/1339615175

http://id.who.int/icd/entity/1283926457

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